EBV infection associated hemophagocytic syndrome as the first manifestation of primary hepatic peripheral T-cell lymphoma: A short report

Primary hepatic lymphoma (PHL) that mainly arises from B lymphocytes has a low-incidence. It is rare for PHL to arise from T lymphocytes. To our best knowledge, this is the first case report in the English literature of a patient with primary hepatic T-cell lymphoma (PHTCL) that takes Epstein-Barr virus infection associated hemophagocytic lymphohistiocytosis (HLH) as the first manifestation. Due to the complexity of clinical manifestations of PHTCL and the diversity of triggering of HLH, follow-up and timely liver or spleen puncture will yield great importance for the final diagnosis of PHTCL especially when HLH as its first manifestation.